A light-inducible protein clustering system for in vivo analysis of α-synuclein aggregation in Parkinson disease

Date

2022

Authors

Bérard, Morgan
Sheta, Razan
Malvaut, Sarah
Rodriguez-Aller, Raquel
Teixeira, Maxime
Idi, Walid
Turmel, Roxanne
Alpaugh, Melanie
Dubois, Marilyn
Dahmene, Manel

Journal Title

Journal ISSN

Volume Title

Publisher

PLoS Biology

Abstract

Neurodegenerative disorders refer to a group of diseases commonly associated with abnormal protein accumulation and aggregation in the central nervous system. However, the exact role of protein aggregation in the pathophysiology of these disorders remains unclear. This gap in knowledge is due to the lack of experimental models that allow for the spatiotemporal control of protein aggregation, and the investigation of early dynamic events associated with inclusion formation. Here, we report on the development of a light-inducible protein aggregation (LIPA) system that enables spatiotemporal control of α-synuclein (α-syn) aggregation into insoluble deposits called Lewy bodies (LBs), the pathological hallmark of Parkinson disease (PD) and other proteinopathies. We demonstrate that LIPA-α-syn inclusions mimic key biochemical, biophysical, and ultrastructural features of authentic LBs observed in PD-diseased brains. In vivo, LIPA-α-syn aggregates compromise nigrostriatal transmission, induce neurodegeneration and PD-like motor impairments. Collectively, our findings provide a new tool for the generation, visualization, and dissection of the role of α-syn aggregation in PD.

Description

We would like to thank Ms. Frédérique Larroquette from McGill University for her technical assistance.

Keywords

neurons, dopaminergics, protein aggregation, midbrain, optogenetics, transfection, neostriatum, confocal microscopy

Citation

Bérard, M., Sheta, R., Malvaut, S., Rodriguez-Aller, R., Teixeira, M., Idi, W., ... Oueslati, A. (2022). A light-inducible protein clustering system for in vivo analysis of α-synuclein aggregation in Parkinson disease. PLoS Biology, 20(3), e3001578. https://doi.org/10.1371/journal.pbio.3001578